Familial Hemophagocytic Lymphohistiocytosis Presenting as Hydrops Fetalis
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چکیده
منابع مشابه
Familial Hemophagocytic Lymphohistiocytosis Presenting as Hydrops Fetalis
Background Familial hemophagocytic lymphohistiocytosis (FLH) is an autosomal recessive disorder of immune regulation that leads to a hyperinflammatory syndrome. Fetal onset FHL is extremely rare and is considered to be the most severe form of FHL. Case We report a preterm case of FHL that presented as hydrops fetalis. The infant was treated with a chemotherapy regimen based on the HLH-2004 prot...
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ژورنال
عنوان ژورنال: American Journal of Perinatology Reports
سال: 2015
ISSN: 2157-6998,2157-7005
DOI: 10.1055/s-0034-1544110